{"id":40843,"date":"2024-06-18T13:26:18","date_gmt":"2024-06-18T11:26:18","guid":{"rendered":"https:\/\/www.stpierre-bru.be\/wereld-sikkelcel-dag\/"},"modified":"2024-06-18T14:28:48","modified_gmt":"2024-06-18T12:28:48","slug":"wereld-sikkelcel-dag","status":"publish","type":"post","link":"https:\/\/www.stpierre-bru.be\/nl\/wereld-sikkelcel-dag\/","title":{"rendered":"Wereld Sikkelcel Dag"},"content":{"rendered":"<p>[et_pb_section fb_built=&#8221;1&#8243; admin_label=&#8221;section&#8221; _builder_version=&#8221;4.16&#8243; global_colors_info=&#8221;{}&#8221;][et_pb_row admin_label=&#8221;row&#8221; _builder_version=&#8221;4.16&#8243; background_size=&#8221;initial&#8221; background_position=&#8221;top_left&#8221; background_repeat=&#8221;repeat&#8221; global_colors_info=&#8221;{}&#8221;][et_pb_column type=&#8221;4_4&#8243; _builder_version=&#8221;4.16&#8243; custom_padding=&#8221;|||&#8221; global_colors_info=&#8221;{}&#8221; custom_padding__hover=&#8221;|||&#8221;][et_pb_text admin_label=&#8221;Text&#8221; _builder_version=&#8221;4.25.2&#8243; text_text_color=&#8221;#000000&#8243; background_size=&#8221;initial&#8221; background_position=&#8221;top_left&#8221; background_repeat=&#8221;repeat&#8221; hover_enabled=&#8221;0&#8243; global_colors_info=&#8221;{}&#8221; sticky_enabled=&#8221;0&#8243;]<\/p>\n<h1 style=\"text-align: center;\"><span style=\"color: #ff9900;\"><strong><span data-contrast=\"auto\" xml:lang=\"FR-BE\" lang=\"FR-BE\" class=\"TextRun SCXW240224337 BCX0\"><span class=\"NormalTextRun SCXW240224337 BCX0\"><span style=\"color: #ff0000;\"><span data-contrast=\"auto\" xml:lang=\"FR-BE\" lang=\"FR-BE\" class=\"TextRun SCXW184230702 BCX0\"><span class=\"NormalTextRun SCXW184230702 BCX0\">19 juni \/ <\/span><span class=\"NormalTextRun SCXW184230702 BCX0\">\u00a0Werelds<\/span><span class=\"NormalTextRun SCXW184230702 BCX0\">ikkelcelziekte<\/span><\/span><span class=\"EOP SCXW184230702 BCX0\" data-ccp-props=\"{\" 201341983=\"\" :0=\"\" 335551550=\"\" :2=\"\" 335551620=\"\" 335559739=\"\" :160=\"\" 335559740=\"\" :279=\"\"><br \/><span data-contrast=\"auto\" lang=\"FR-BE\" class=\"TextRun SCXW99836974 BCX0\" xml:lang=\"FR-BE\"><span class=\"NormalTextRun SCXW99836974 BCX0\">Een niet zo zeldzame Ziekte <\/span><span class=\"NormalTextRun SCXW99836974 BCX0\">&#8230;<\/span><br \/><\/span><span class=\"EOP SCXW99836974 BCX0\" data-ccp-props=\"{\" 201341983=\"\" :0=\"\" 335551550=\"\" :2=\"\" 335551620=\"\" 335559739=\"\" :160=\"\" 335559740=\"\" :279=\"\"> <\/span><br \/><\/span><\/span><\/span><\/span><\/strong><\/span><\/h1>\n<p><strong><span data-contrast=\"auto\" xml:lang=\"FR-BE\" lang=\"FR-BE\" class=\"TextRun SCXW261580485 BCX0\"><span class=\"NormalTextRun SCXW261580485 BCX0\">Definitie van de ziekte<\/span><\/span><\/strong><\/p>\n<p><span data-contrast=\"auto\" xml:lang=\"FR-BE\" lang=\"FR-BE\" class=\"TextRun SCXW192605497 BCX0\"><span class=\"NormalTextRun SCXW192605497 BCX0\"><span data-contrast=\"none\" xml:lang=\"FR-BE\" lang=\"FR-BE\" class=\"TextRun SCXW104591888 BCX0\"><span class=\"NormalTextRun SCXW104591888 BCX0\"><span data-contrast=\"none\" xml:lang=\"NL-BE\" lang=\"NL-BE\" class=\"TextRun SCXW131380018 BCX0\"><span class=\"NormalTextRun SCXW131380018 BCX0\">Sikkelcelanemie is een genetische ziekte die de rode bloedcellen aantast. Het is momenteel de meest voorkomende genetische ziekte ter wereld. In Brussel telt men 1 geval per 1400 geboorten. Het is een systemische ziekte die een impact kan hebben op elk orgaan in het lichaam: de hersenen, de longen, het hart, de nieren, de milt, de lever, de botten, de ogen en de oren in het bijzonder.<\/span><\/span><span class=\"EOP SCXW131380018 BCX0\" data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/span><strong><br \/><span class=\"NormalTextRun SCXW104591888 BCX0\"><\/span><\/strong><\/span><\/span><\/span><\/p>\n<p><strong><span data-contrast=\"auto\" xml:lang=\"FR-BE\" lang=\"FR-BE\" class=\"TextRun SCXW261580485 BCX0\"><span class=\"NormalTextRun SCXW261580485 BCX0\"><span data-contrast=\"auto\" xml:lang=\"NL-BE\" lang=\"NL-BE\" class=\"TextRun SCXW173470442 BCX0\"><span class=\"NormalTextRun SCXW173470442 BCX0\">Symptomen van de ziekte<br \/><\/span><\/span><\/span><\/span><\/strong><span data-contrast=\"none\">Sikkelcelziekte uit zich in verschillende symptomen:\u00a0<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<ul>\n<li data-leveltext=\"-\" data-font=\"Aptos\" data-listid=\"4\" data-list-defn-props=\"{&quot;335552541&quot;:1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769226&quot;:&quot;Aptos&quot;,&quot;469769242&quot;:[8226],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;-&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" aria-setsize=\"-1\" data-aria-posinset=\"1\" data-aria-level=\"1\"><span data-contrast=\"none\">Chronische bloedarmoede verergerd in acute situaties<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/li>\n<\/ul>\n<ul>\n<li data-leveltext=\"-\" data-font=\"Aptos\" data-listid=\"3\" data-list-defn-props=\"{&quot;335552541&quot;:1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769226&quot;:&quot;Aptos&quot;,&quot;469769242&quot;:[8226],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;-&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" aria-setsize=\"-1\" data-aria-posinset=\"1\" data-aria-level=\"1\"><span data-contrast=\"none\">Grotere vatbaarheid voor invasieve bacteri\u00eble infecties<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/li>\n<\/ul>\n<ul>\n<li data-leveltext=\"-\" data-font=\"Aptos\" data-listid=\"2\" data-list-defn-props=\"{&quot;335552541&quot;:1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769226&quot;:&quot;Aptos&quot;,&quot;469769242&quot;:[8226],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;-&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" aria-setsize=\"-1\" data-aria-posinset=\"1\" data-aria-level=\"1\"><span data-contrast=\"none\">Pijnlijke aanvallen veroorzaakt door een mogelijke vaso-occlusie van het bloed in alle organen.\u00a0<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/li>\n<\/ul>\n<ul>\n<li data-leveltext=\"-\" data-font=\"Aptos\" data-listid=\"1\" data-list-defn-props=\"{&quot;335552541&quot;:1,&quot;335559685&quot;:720,&quot;335559991&quot;:360,&quot;469769226&quot;:&quot;Aptos&quot;,&quot;469769242&quot;:[8226],&quot;469777803&quot;:&quot;left&quot;,&quot;469777804&quot;:&quot;-&quot;,&quot;469777815&quot;:&quot;hybridMultilevel&quot;}\" aria-setsize=\"-1\" data-aria-posinset=\"1\" data-aria-level=\"1\"><span data-contrast=\"none\">Chronische vaatschade<\/span><span data-contrast=\"auto\">, beroertes,<\/span><span data-contrast=\"none\"> verlies van gezichtsvermogen\u00a0<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/li>\n<\/ul>\n<p><span data-contrast=\"none\">Deze symptomen zijn niet altijd zichtbaar, maar daarom niet minder intens. Het is dan ook essentieel om hiermee rekening te houden als u de ziekte en het lijden van de getroffen pati\u00ebnten wilt begrijpen.\u00a0<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\"><\/span><\/p>\n<p>&nbsp;<\/p>\n<p><b><span data-contrast=\"auto\">Overdracht van de ziekte<\/span><\/b><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\"><br \/><\/span><span data-contrast=\"auto\">Sikkelcelziekte is een autosomaal (gekoppeld aan een niet-geslachtschromosoom) recessief overervende aandoening. Er is 25% kans dat een kind de ziekte heeft als beide ouders drager zijn van het aangetaste gen. Het is waar dat de ziekte vroeger vooral bepaalde bevolkingsgroepen trof, maar door de vermenging van bevolkingsgroepen kan tegenwoordig iedereen worden getroffen. Het is echter geen infectieziekte: het is niet besmettelijk door contact of transfusie.<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><b><span data-contrast=\"auto\">Opsporing<\/span><\/b><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\"><br \/><\/span><span data-contrast=\"auto\">Dragers zijn over het algemeen asymptomatisch en hun bloedtests zijn volledig normaal. De ziekte kan dan uitsluitend worden opgespoord via een hemoglobine-elektroforese. Dit maakt het extra moeilijk om te onderzoeken of iemand drager is. Een sikkelcelpati\u00ebnt met Hb SC kan een normaal Hb hebben (met een microcytose). Het is daarom van vitaal belang om in bepaalde situaties opsporing te overwegen: vermoeden van een sikkelcelpati\u00ebnt, optreden van symptomen, voorkomen van een toekomstige sikkelcelpati\u00ebnt, kinderwens, enz. Dit gebeurt soms systematisch bij bepaalde specialisten (zoals bij gynaecologie in het UMC Sint-Pieter, waar opsporing van de partner vereist is). Maar soms is het nodig om beroep te doen op uw huisarts als u hierover vragen hebt.<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\"><\/span><\/p>\n<p><b><span data-contrast=\"auto\">Bij het UMC Sint-Pieter<\/span><\/b><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">Deze zeldzame en complexe ziekte vereist behandeling in gespecialiseerde centra. In het UMC Sint-Pieter behandelen we deze ziekte en de pati\u00ebnten die eraan lijden al heel lang. Daarom besteden we veel aandacht aan hun lijden en de chronische complicaties die zij kunnen oplopen.<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\"><\/span><\/p>\n<p><b><span data-contrast=\"auto\">Bloeddonatie: een noodzaak<\/span><\/b><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"none\">Sikkelcelanemie is een chronische ziekte waarvoor momenteel geen eenvoudige behandeling bestaat. Om de ziekte te genezen is een beenmergtransplantatie nodig waarbij beenmerg van een HLA-compatibele donor wordt gebruikt. In feite heeft slechts 20% van de pati\u00ebnten een beenmergdonor. Ook gentherapie ligt in het verschiet. Er worden eveneens bepaalde technieken ontwikkeld voor transplantaties met behulp van semi-compatibele donoren bij volwassenen.\u00a0<\/span><span data-contrast=\"auto\">\u00a0<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-contrast=\"auto\">Zoals bij veel bloedziekten hebben pati\u00ebnten met sikkelcelziekte bloeddonaties nodig met bloed dat zo veel mogelijk lijkt op dat van hun. Wereldsikkelceldag is daarom het perfecte moment om iedereen eraan te herinneren dat bloeddonatie levens kan redden en dat het belangrijk is dat iedereen zich betrokken voelt.\u00a0<\/span><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p><span data-ccp-props=\"{&quot;201341983&quot;:0,&quot;335559739&quot;:160,&quot;335559740&quot;:279}\">\u00a0<\/span><\/p>\n<p>[\/et_pb_text][\/et_pb_column][\/et_pb_row][\/et_pb_section]<\/p>\n","protected":false},"excerpt":{"rendered":"<p>19 juni \/ \u00a0WereldsikkelcelziekteEen niet zo zeldzame Ziekte &#8230; Definitie van de ziekte Sikkelcelanemie is een genetische ziekte die de rode bloedcellen aantast. Het is momenteel de meest voorkomende genetische [&hellip;]<\/p>\n","protected":false},"author":9,"featured_media":40828,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_acf_changed":false,"_et_pb_use_builder":"on","_et_pb_old_content":"","_et_gb_content_width":"","_price":"","_stock":"","_tribe_ticket_header":"","_tribe_default_ticket_provider":"","_tribe_ticket_capacity":"0","_ticket_start_date":"","_ticket_end_date":"","_tribe_ticket_show_description":"","_tribe_ticket_show_not_going":false,"_tribe_ticket_use_global_stock":"","_tribe_ticket_global_stock_level":"","_global_stock_mode":"","_global_stock_cap":"","_tribe_rsvp_for_event":"","_tribe_ticket_going_count":"","_tribe_ticket_not_going_count":"","_tribe_tickets_list":"[]","_tribe_ticket_has_attendee_info_fields":false,"footnotes":""},"categories":[45],"tags":[1697],"class_list":["post-40843","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-geen-onderdeel-van-een-categorie","tag-drepanocytose-nl"],"acf":[],"yoast_head":"<!-- This site is optimized with the Yoast SEO plugin v27.8 - https:\/\/yoast.com\/product\/yoast-seo-wordpress\/ -->\n<title>Wereld Sikkelcel Dag - CHU Saint-Pierre | UMC Sint-Pieter<\/title>\n<meta name=\"description\" content=\"Deze genetische ziekte, die de rode bloedcellen aantast, is momenteel de meest voorkomende genetische ziekte ter wereld. In Brussel is er 1 geval op 1400 geboorten. Het is een systemische ziekte die elk orgaan in het lichaam kan aantasten, waaronder de hersenen, longen, hart, nieren, milt, lever, botten, ogen en oren.\" \/>\n<meta name=\"robots\" content=\"index, follow, max-snippet:-1, max-image-preview:large, max-video-preview:-1\" \/>\n<link rel=\"canonical\" href=\"https:\/\/www.stpierre-bru.be\/nl\/wereld-sikkelcel-dag\/\" \/>\n<meta property=\"og:locale\" content=\"nl_NL\" \/>\n<meta property=\"og:type\" content=\"article\" \/>\n<meta property=\"og:title\" content=\"Wereld Sikkelcel Dag - CHU Saint-Pierre | UMC Sint-Pieter\" \/>\n<meta property=\"og:description\" content=\"Deze genetische ziekte, die de rode bloedcellen aantast, is momenteel de meest voorkomende genetische ziekte ter wereld. In Brussel is er 1 geval op 1400 geboorten. 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